A case of porphyria cutanea tarda in association with idiopathic myelofibrosis and CREST syndrome
Lee, S.C. ; Yun, S.J. ; Lee, J-B. ; Lee, S-S. ; Won, Y.H.
Oxford, UK : Blackwell Science Ltd
Published 2001
Oxford, UK : Blackwell Science Ltd
Published 2001
| ISSN: |
1365-2133
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|---|---|
| Source: |
Blackwell Publishing Journal Backfiles 1879-2005
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| Topics: |
Medicine
|
| Notes: |
We report a 56-year-old Korean woman with porphyria cutanea tarda (PCT), showing multiple scarring bullae and hypertrichosis on sun-exposed areas of skin with postinflammatory hyperpigmentation. Sclerodermoid changes were also found on both hands, the face and neck. The patient had suffered from CREST syndrome, manifesting with Raynaud’s phenomenon and sclerodactyly, for more than 15 years. Anticentromere antibody was positive. She had presented with splenomegaly 3 years before the development of PCT, and was diagnosed as having idiopathic myelofibrosis, based on bone marrow biopsy. In summary, she had had CREST syndrome for 15 years and later developed idiopathic myelofibrosis and PCT. This is the first reported case of PCT in association with idiopathic myelofibrosis and CREST syndrome.
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| Type of Medium: |
Electronic Resource
|
| URL: |
| _version_ | 1798290095297527808 |
|---|---|
| autor | Lee, S.C. Yun, S.J. Lee, J-B. Lee, S-S. Won, Y.H. |
| autorsonst | Lee, S-S. Won, Y.H. |
| book_url | http://dx.doi.org/10.1046/j.1365-2133.2001.03971.x |
| datenlieferant | nat_lic_papers |
| hauptsatz | hsatz_simple |
| identnr | NLZ242132537 |
| insertion_date | 2012-04-27 |
| issn | 1365-2133 |
| journal_name | British journal of dermatology |
| materialart | 1 |
| notes | We report a 56-year-old Korean woman with porphyria cutanea tarda (PCT), showing multiple scarring bullae and hypertrichosis on sun-exposed areas of skin with postinflammatory hyperpigmentation. Sclerodermoid changes were also found on both hands, the face and neck. The patient had suffered from CREST syndrome, manifesting with Raynaud’s phenomenon and sclerodactyly, for more than 15 years. Anticentromere antibody was positive. She had presented with splenomegaly 3 years before the development of PCT, and was diagnosed as having idiopathic myelofibrosis, based on bone marrow biopsy. In summary, she had had CREST syndrome for 15 years and later developed idiopathic myelofibrosis and PCT. This is the first reported case of PCT in association with idiopathic myelofibrosis and CREST syndrome. |
| package_name | Blackwell Publishing |
| publikationsjahr_anzeige | 2001 |
| publikationsjahr_facette | 2001 |
| publikationsjahr_intervall | 7999:2000-2004 |
| publikationsjahr_sort | 2001 |
| publikationsort | Oxford, UK |
| publisher | Blackwell Science Ltd |
| reference | 144 (2001), S. 0 |
| search_space | articles |
| shingle_author_1 | Lee, S.C. Yun, S.J. Lee, J-B. Lee, S-S. Won, Y.H. |
| shingle_author_2 | Lee, S.C. Yun, S.J. Lee, J-B. Lee, S-S. Won, Y.H. |
| shingle_author_3 | Lee, S.C. Yun, S.J. Lee, J-B. Lee, S-S. Won, Y.H. |
| shingle_author_4 | Lee, S.C. Yun, S.J. Lee, J-B. Lee, S-S. Won, Y.H. |
| shingle_catch_all_1 | Lee, S.C. Yun, S.J. Lee, J-B. Lee, S-S. Won, Y.H. A case of porphyria cutanea tarda in association with idiopathic myelofibrosis and CREST syndrome Blackwell Science Ltd We report a 56-year-old Korean woman with porphyria cutanea tarda (PCT), showing multiple scarring bullae and hypertrichosis on sun-exposed areas of skin with postinflammatory hyperpigmentation. Sclerodermoid changes were also found on both hands, the face and neck. The patient had suffered from CREST syndrome, manifesting with Raynaud’s phenomenon and sclerodactyly, for more than 15 years. Anticentromere antibody was positive. She had presented with splenomegaly 3 years before the development of PCT, and was diagnosed as having idiopathic myelofibrosis, based on bone marrow biopsy. In summary, she had had CREST syndrome for 15 years and later developed idiopathic myelofibrosis and PCT. This is the first reported case of PCT in association with idiopathic myelofibrosis and CREST syndrome. 1365-2133 13652133 |
| shingle_catch_all_2 | Lee, S.C. Yun, S.J. Lee, J-B. Lee, S-S. Won, Y.H. A case of porphyria cutanea tarda in association with idiopathic myelofibrosis and CREST syndrome Blackwell Science Ltd We report a 56-year-old Korean woman with porphyria cutanea tarda (PCT), showing multiple scarring bullae and hypertrichosis on sun-exposed areas of skin with postinflammatory hyperpigmentation. Sclerodermoid changes were also found on both hands, the face and neck. The patient had suffered from CREST syndrome, manifesting with Raynaud’s phenomenon and sclerodactyly, for more than 15 years. Anticentromere antibody was positive. She had presented with splenomegaly 3 years before the development of PCT, and was diagnosed as having idiopathic myelofibrosis, based on bone marrow biopsy. In summary, she had had CREST syndrome for 15 years and later developed idiopathic myelofibrosis and PCT. This is the first reported case of PCT in association with idiopathic myelofibrosis and CREST syndrome. 1365-2133 13652133 |
| shingle_catch_all_3 | Lee, S.C. Yun, S.J. Lee, J-B. Lee, S-S. Won, Y.H. A case of porphyria cutanea tarda in association with idiopathic myelofibrosis and CREST syndrome Blackwell Science Ltd We report a 56-year-old Korean woman with porphyria cutanea tarda (PCT), showing multiple scarring bullae and hypertrichosis on sun-exposed areas of skin with postinflammatory hyperpigmentation. Sclerodermoid changes were also found on both hands, the face and neck. The patient had suffered from CREST syndrome, manifesting with Raynaud’s phenomenon and sclerodactyly, for more than 15 years. Anticentromere antibody was positive. She had presented with splenomegaly 3 years before the development of PCT, and was diagnosed as having idiopathic myelofibrosis, based on bone marrow biopsy. In summary, she had had CREST syndrome for 15 years and later developed idiopathic myelofibrosis and PCT. This is the first reported case of PCT in association with idiopathic myelofibrosis and CREST syndrome. 1365-2133 13652133 |
| shingle_catch_all_4 | Lee, S.C. Yun, S.J. Lee, J-B. Lee, S-S. Won, Y.H. A case of porphyria cutanea tarda in association with idiopathic myelofibrosis and CREST syndrome Blackwell Science Ltd We report a 56-year-old Korean woman with porphyria cutanea tarda (PCT), showing multiple scarring bullae and hypertrichosis on sun-exposed areas of skin with postinflammatory hyperpigmentation. Sclerodermoid changes were also found on both hands, the face and neck. The patient had suffered from CREST syndrome, manifesting with Raynaud’s phenomenon and sclerodactyly, for more than 15 years. Anticentromere antibody was positive. She had presented with splenomegaly 3 years before the development of PCT, and was diagnosed as having idiopathic myelofibrosis, based on bone marrow biopsy. In summary, she had had CREST syndrome for 15 years and later developed idiopathic myelofibrosis and PCT. This is the first reported case of PCT in association with idiopathic myelofibrosis and CREST syndrome. 1365-2133 13652133 |
| shingle_title_1 | A case of porphyria cutanea tarda in association with idiopathic myelofibrosis and CREST syndrome |
| shingle_title_2 | A case of porphyria cutanea tarda in association with idiopathic myelofibrosis and CREST syndrome |
| shingle_title_3 | A case of porphyria cutanea tarda in association with idiopathic myelofibrosis and CREST syndrome |
| shingle_title_4 | A case of porphyria cutanea tarda in association with idiopathic myelofibrosis and CREST syndrome |
| sigel_instance_filter | dkfz geomar wilbert ipn albert |
| source_archive | Blackwell Publishing Journal Backfiles 1879-2005 |
| timestamp | 2024-05-06T08:11:17.064Z |
| titel | A case of porphyria cutanea tarda in association with idiopathic myelofibrosis and CREST syndrome |
| titel_suche | A case of porphyria cutanea tarda in association with idiopathic myelofibrosis and CREST syndrome |
| topic | WW-YZ |
| uid | nat_lic_papers_NLZ242132537 |