Increased chloride efflux in fibroblasts from X-linked muscular dystrophies and clones from Duchenne carriers
| ISSN: |
0014-5793
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|---|---|
| Keywords: |
(Human) ; Becker muscular dystrophy ; Cl^- efflux ; Duchenne muscular dystrophy ; Emery-Dreifuss muscular dystrophy ; Fibroblast ; X-linked muscular dystrophy
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| Source: |
Elsevier Journal Backfiles on ScienceDirect 1907 - 2002
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| Topics: |
Biology
Chemistry and Pharmacology
Physics
|
| Type of Medium: |
Electronic Resource
|
| URL: |
| _version_ | 1798290828192382977 |
|---|---|
| autor | Rugolo, M. Rocchi, M. Lenaz, G. Romeo, G. |
| autorsonst | Rugolo, M. Rocchi, M. Lenaz, G. Romeo, G. |
| book_url | http://linkinghub.elsevier.com/retrieve/pii/0014-5793(87)81367-4 |
| datenlieferant | nat_lic_papers |
| fussnote | Previous studies have suggested an increased chloride membrane permeability in Duchenne muscular dystrophy (DMD) fibroblasts. We report that an increased chloride efflux with respect to controls is present not only in fibroblasts from DMD, but also from two other X-linked muscular dystrophies, Becker and Emery-Dreifuss, as well as in clones from DMD carrier females. The latter observation suggests that, at least in DMD, the increased chloride efflux phenotype might be subject to lyonization. |
| hauptsatz | hsatz_simple |
| identnr | NLZ173296459 |
| issn | 0014-5793 |
| journal_name | FEBS Letters |
| materialart | 1 |
| package_name | Elsevier |
| publikationsort | Amsterdam |
| publisher | Elsevier |
| reference | 212 (1987), S. 313-316 |
| schlagwort | (Human) Becker muscular dystrophy Cl^- efflux Duchenne muscular dystrophy Emery-Dreifuss muscular dystrophy Fibroblast X-linked muscular dystrophy |
| search_space | articles |
| shingle_author_1 | Rugolo, M. Rocchi, M. Lenaz, G. Romeo, G. |
| shingle_author_2 | Rugolo, M. Rocchi, M. Lenaz, G. Romeo, G. |
| shingle_author_3 | Rugolo, M. Rocchi, M. Lenaz, G. Romeo, G. |
| shingle_author_4 | Rugolo, M. Rocchi, M. Lenaz, G. Romeo, G. |
| shingle_catch_all_1 | Rugolo, M. Rocchi, M. Lenaz, G. Romeo, G. Increased chloride efflux in fibroblasts from X-linked muscular dystrophies and clones from Duchenne carriers (Human) Becker muscular dystrophy Cl^- efflux Duchenne muscular dystrophy Emery-Dreifuss muscular dystrophy Fibroblast X-linked muscular dystrophy (Human) Becker muscular dystrophy Cl^- efflux Duchenne muscular dystrophy Emery-Dreifuss muscular dystrophy Fibroblast X-linked muscular dystrophy 0014-5793 00145793 Elsevier |
| shingle_catch_all_2 | Rugolo, M. Rocchi, M. Lenaz, G. Romeo, G. Increased chloride efflux in fibroblasts from X-linked muscular dystrophies and clones from Duchenne carriers (Human) Becker muscular dystrophy Cl^- efflux Duchenne muscular dystrophy Emery-Dreifuss muscular dystrophy Fibroblast X-linked muscular dystrophy (Human) Becker muscular dystrophy Cl^- efflux Duchenne muscular dystrophy Emery-Dreifuss muscular dystrophy Fibroblast X-linked muscular dystrophy 0014-5793 00145793 Elsevier |
| shingle_catch_all_3 | Rugolo, M. Rocchi, M. Lenaz, G. Romeo, G. Increased chloride efflux in fibroblasts from X-linked muscular dystrophies and clones from Duchenne carriers (Human) Becker muscular dystrophy Cl^- efflux Duchenne muscular dystrophy Emery-Dreifuss muscular dystrophy Fibroblast X-linked muscular dystrophy (Human) Becker muscular dystrophy Cl^- efflux Duchenne muscular dystrophy Emery-Dreifuss muscular dystrophy Fibroblast X-linked muscular dystrophy 0014-5793 00145793 Elsevier |
| shingle_catch_all_4 | Rugolo, M. Rocchi, M. Lenaz, G. Romeo, G. Increased chloride efflux in fibroblasts from X-linked muscular dystrophies and clones from Duchenne carriers (Human) Becker muscular dystrophy Cl^- efflux Duchenne muscular dystrophy Emery-Dreifuss muscular dystrophy Fibroblast X-linked muscular dystrophy (Human) Becker muscular dystrophy Cl^- efflux Duchenne muscular dystrophy Emery-Dreifuss muscular dystrophy Fibroblast X-linked muscular dystrophy 0014-5793 00145793 Elsevier |
| shingle_title_1 | Increased chloride efflux in fibroblasts from X-linked muscular dystrophies and clones from Duchenne carriers |
| shingle_title_2 | Increased chloride efflux in fibroblasts from X-linked muscular dystrophies and clones from Duchenne carriers |
| shingle_title_3 | Increased chloride efflux in fibroblasts from X-linked muscular dystrophies and clones from Duchenne carriers |
| shingle_title_4 | Increased chloride efflux in fibroblasts from X-linked muscular dystrophies and clones from Duchenne carriers |
| sigel_instance_filter | dkfz geomar wilbert ipn albert fhp |
| source_archive | Elsevier Journal Backfiles on ScienceDirect 1907 - 2002 |
| timestamp | 2024-05-06T08:22:56.190Z |
| titel | Increased chloride efflux in fibroblasts from X-linked muscular dystrophies and clones from Duchenne carriers |
| titel_suche | Increased chloride efflux in fibroblasts from X-linked muscular dystrophies and clones from Duchenne carriers Previous studies have suggested an increased chloride membrane permeability in Duchenne muscular dystrophy (DMD) fibroblasts. We report that an increased chloride efflux with respect to controls is present not only in fibroblasts from DMD, but also from two other X-linked muscular dystrophies, Becker and Emery-Dreifuss, as well as in clones from DMD carrier females. The latter observation suggests that, at least in DMD, the increased chloride efflux phenotype might be subject to lyonization. |
| topic | W V U |
| uid | nat_lic_papers_NLZ173296459 |