Pulmonary alveolar microlithiasis: Review of Italian reports
| ISSN: |
1573-7284
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|---|---|
| Keywords: |
Calculi ; Case reports ; Diagnosis ; Epidemiology ; Lung diseases ; Review article
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| Source: |
Springer Online Journal Archives 1860-2000
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| Topics: |
Medicine
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| Notes: |
Abstract Pulmonary alveolar microlithiasis (PAM) is a rare disease of unknown etiology, characterized by the presence of calcific concretions in the alveolar spaces. A familial occurrence is frequently found so that an inherited trait is thought to be involved. The chest X-ray is characterized by a ‘sandstorm’ picture while the clinical state undergoes to a slow and progressive impairment resulting in respiratory failure at the end stage. We have reviewed the Italian literature of the past 50 years detecting 48 case-reports of PAM (19 males and 29 females). Only 20 out of them were documented in international journals. A familial occurence of 43.7% was found and 18 patients were under age fifteen. There was a prevalence in the female sex (60.4%) and in the second decade of life. Chest X-ray was the most important tool to diagnose PAM revealing the characteristic picture in all patient. Bronchoalveolar lavage (BAL) and open lung biopsy respectively show the characteristic calcospherites in the recovered fluid (BALF) and in the alveolar spaces. About 300 cases of PAM are reported in the international literature. We believe these data are probably underestimated because many case-reports are not published in international literature.
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| Type of Medium: |
Electronic Resource
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| URL: |
| _version_ | 1798296900899700737 |
|---|---|
| autor | Mariotta, S. Guidi, L. Papale, M. Ricci, A. Bisetti, A. |
| autorsonst | Mariotta, S. Guidi, L. Papale, M. Ricci, A. Bisetti, A. |
| book_url | http://dx.doi.org/10.1023/A:1007399812798 |
| datenlieferant | nat_lic_papers |
| hauptsatz | hsatz_simple |
| identnr | NLM193240327 |
| issn | 1573-7284 |
| journal_name | European journal of epidemiology |
| materialart | 1 |
| notes | Abstract Pulmonary alveolar microlithiasis (PAM) is a rare disease of unknown etiology, characterized by the presence of calcific concretions in the alveolar spaces. A familial occurrence is frequently found so that an inherited trait is thought to be involved. The chest X-ray is characterized by a ‘sandstorm’ picture while the clinical state undergoes to a slow and progressive impairment resulting in respiratory failure at the end stage. We have reviewed the Italian literature of the past 50 years detecting 48 case-reports of PAM (19 males and 29 females). Only 20 out of them were documented in international journals. A familial occurence of 43.7% was found and 18 patients were under age fifteen. There was a prevalence in the female sex (60.4%) and in the second decade of life. Chest X-ray was the most important tool to diagnose PAM revealing the characteristic picture in all patient. Bronchoalveolar lavage (BAL) and open lung biopsy respectively show the characteristic calcospherites in the recovered fluid (BALF) and in the alveolar spaces. About 300 cases of PAM are reported in the international literature. We believe these data are probably underestimated because many case-reports are not published in international literature. |
| package_name | Springer |
| publikationsjahr_anzeige | 1997 |
| publikationsjahr_facette | 1997 |
| publikationsjahr_intervall | 8004:1995-1999 |
| publikationsjahr_sort | 1997 |
| publisher | Springer |
| reference | 13 (1997), S. 587-590 |
| schlagwort | Calculi Case reports Diagnosis Epidemiology Lung diseases Review article |
| search_space | articles |
| shingle_author_1 | Mariotta, S. Guidi, L. Papale, M. Ricci, A. Bisetti, A. |
| shingle_author_2 | Mariotta, S. Guidi, L. Papale, M. Ricci, A. Bisetti, A. |
| shingle_author_3 | Mariotta, S. Guidi, L. Papale, M. Ricci, A. Bisetti, A. |
| shingle_author_4 | Mariotta, S. Guidi, L. Papale, M. Ricci, A. Bisetti, A. |
| shingle_catch_all_1 | Mariotta, S. Guidi, L. Papale, M. Ricci, A. Bisetti, A. Pulmonary alveolar microlithiasis: Review of Italian reports Calculi Case reports Diagnosis Epidemiology Lung diseases Review article Calculi Case reports Diagnosis Epidemiology Lung diseases Review article Abstract Pulmonary alveolar microlithiasis (PAM) is a rare disease of unknown etiology, characterized by the presence of calcific concretions in the alveolar spaces. A familial occurrence is frequently found so that an inherited trait is thought to be involved. The chest X-ray is characterized by a ‘sandstorm’ picture while the clinical state undergoes to a slow and progressive impairment resulting in respiratory failure at the end stage. We have reviewed the Italian literature of the past 50 years detecting 48 case-reports of PAM (19 males and 29 females). Only 20 out of them were documented in international journals. A familial occurence of 43.7% was found and 18 patients were under age fifteen. There was a prevalence in the female sex (60.4%) and in the second decade of life. Chest X-ray was the most important tool to diagnose PAM revealing the characteristic picture in all patient. Bronchoalveolar lavage (BAL) and open lung biopsy respectively show the characteristic calcospherites in the recovered fluid (BALF) and in the alveolar spaces. About 300 cases of PAM are reported in the international literature. We believe these data are probably underestimated because many case-reports are not published in international literature. 1573-7284 15737284 Springer |
| shingle_catch_all_2 | Mariotta, S. Guidi, L. Papale, M. Ricci, A. Bisetti, A. Pulmonary alveolar microlithiasis: Review of Italian reports Calculi Case reports Diagnosis Epidemiology Lung diseases Review article Calculi Case reports Diagnosis Epidemiology Lung diseases Review article Abstract Pulmonary alveolar microlithiasis (PAM) is a rare disease of unknown etiology, characterized by the presence of calcific concretions in the alveolar spaces. A familial occurrence is frequently found so that an inherited trait is thought to be involved. The chest X-ray is characterized by a ‘sandstorm’ picture while the clinical state undergoes to a slow and progressive impairment resulting in respiratory failure at the end stage. We have reviewed the Italian literature of the past 50 years detecting 48 case-reports of PAM (19 males and 29 females). Only 20 out of them were documented in international journals. A familial occurence of 43.7% was found and 18 patients were under age fifteen. There was a prevalence in the female sex (60.4%) and in the second decade of life. Chest X-ray was the most important tool to diagnose PAM revealing the characteristic picture in all patient. Bronchoalveolar lavage (BAL) and open lung biopsy respectively show the characteristic calcospherites in the recovered fluid (BALF) and in the alveolar spaces. About 300 cases of PAM are reported in the international literature. We believe these data are probably underestimated because many case-reports are not published in international literature. 1573-7284 15737284 Springer |
| shingle_catch_all_3 | Mariotta, S. Guidi, L. Papale, M. Ricci, A. Bisetti, A. Pulmonary alveolar microlithiasis: Review of Italian reports Calculi Case reports Diagnosis Epidemiology Lung diseases Review article Calculi Case reports Diagnosis Epidemiology Lung diseases Review article Abstract Pulmonary alveolar microlithiasis (PAM) is a rare disease of unknown etiology, characterized by the presence of calcific concretions in the alveolar spaces. A familial occurrence is frequently found so that an inherited trait is thought to be involved. The chest X-ray is characterized by a ‘sandstorm’ picture while the clinical state undergoes to a slow and progressive impairment resulting in respiratory failure at the end stage. We have reviewed the Italian literature of the past 50 years detecting 48 case-reports of PAM (19 males and 29 females). Only 20 out of them were documented in international journals. A familial occurence of 43.7% was found and 18 patients were under age fifteen. There was a prevalence in the female sex (60.4%) and in the second decade of life. Chest X-ray was the most important tool to diagnose PAM revealing the characteristic picture in all patient. Bronchoalveolar lavage (BAL) and open lung biopsy respectively show the characteristic calcospherites in the recovered fluid (BALF) and in the alveolar spaces. About 300 cases of PAM are reported in the international literature. We believe these data are probably underestimated because many case-reports are not published in international literature. 1573-7284 15737284 Springer |
| shingle_catch_all_4 | Mariotta, S. Guidi, L. Papale, M. Ricci, A. Bisetti, A. Pulmonary alveolar microlithiasis: Review of Italian reports Calculi Case reports Diagnosis Epidemiology Lung diseases Review article Calculi Case reports Diagnosis Epidemiology Lung diseases Review article Abstract Pulmonary alveolar microlithiasis (PAM) is a rare disease of unknown etiology, characterized by the presence of calcific concretions in the alveolar spaces. A familial occurrence is frequently found so that an inherited trait is thought to be involved. The chest X-ray is characterized by a ‘sandstorm’ picture while the clinical state undergoes to a slow and progressive impairment resulting in respiratory failure at the end stage. We have reviewed the Italian literature of the past 50 years detecting 48 case-reports of PAM (19 males and 29 females). Only 20 out of them were documented in international journals. A familial occurence of 43.7% was found and 18 patients were under age fifteen. There was a prevalence in the female sex (60.4%) and in the second decade of life. Chest X-ray was the most important tool to diagnose PAM revealing the characteristic picture in all patient. Bronchoalveolar lavage (BAL) and open lung biopsy respectively show the characteristic calcospherites in the recovered fluid (BALF) and in the alveolar spaces. About 300 cases of PAM are reported in the international literature. We believe these data are probably underestimated because many case-reports are not published in international literature. 1573-7284 15737284 Springer |
| shingle_title_1 | Pulmonary alveolar microlithiasis: Review of Italian reports |
| shingle_title_2 | Pulmonary alveolar microlithiasis: Review of Italian reports |
| shingle_title_3 | Pulmonary alveolar microlithiasis: Review of Italian reports |
| shingle_title_4 | Pulmonary alveolar microlithiasis: Review of Italian reports |
| sigel_instance_filter | dkfz geomar wilbert ipn albert fhp |
| source_archive | Springer Online Journal Archives 1860-2000 |
| timestamp | 2024-05-06T09:59:27.174Z |
| titel | Pulmonary alveolar microlithiasis: Review of Italian reports |
| titel_suche | Pulmonary alveolar microlithiasis: Review of Italian reports |
| topic | WW-YZ |
| uid | nat_lic_papers_NLM193240327 |